Congenital portosystemic vascular malformations.
Semin Pediatr Surg
; 21(3): 233-44, 2012 Aug.
Article
in En
| MEDLINE
| ID: mdl-22800976
ABSTRACT
Congenital portosystemic shunts are developmental abnormalities of the portal venous system resulting in the diversion of portal blood away from the liver to the systemic venous system. Such malformations are believed to come from an insult occurring between the fourth and eighth week of gestation during the development of hepatic and systemic venous systems, and could explain their frequent association with cardiac and other vascular anomalies. They are currently categorized into end-to-side shunts (type I) or side-to-side shunts (type II). This article aims to review the common symptoms and complications encountered in congenital portosystemic shunts, the surgical and endovascular treatment, and the role of liver transplantation in this disease. We will also focus on the current controversies and the areas where there is potential for future studies.
Full text:
1
Collection:
01-internacional
Database:
MEDLINE
Main subject:
Portal Vein
/
Vascular Malformations
Type of study:
Diagnostic_studies
Limits:
Humans
Language:
En
Journal:
Semin Pediatr Surg
Journal subject:
PEDIATRIA
Year:
2012
Document type:
Article
Affiliation country: