Meandering right pulmonary vein associated with severe and progressive "idiopathic-like" pulmonary hypertensive vascular disease.
Cardiol Young
; 26(3): 615-8, 2016 Mar.
Article
in En
| MEDLINE
| ID: mdl-26374461
ABSTRACT
Congenital anomalies of the pulmonary veins are rare. Meandering right pulmonary vein, considered a part of the Scimitar syndrome spectrum, is often an incidental finding during chest imaging. We present the case of a 4-year-old girl diagnosed with meandering pulmonary vein, who developed pulmonary hypertensive disease with an aggressive course, in spite of absence of hypoxia or elevated pulmonary wedge pressure.
Key words
Full text:
1
Collection:
01-internacional
Database:
MEDLINE
Main subject:
Pulmonary Veins
/
Hypertension, Pulmonary
Type of study:
Diagnostic_studies
/
Risk_factors_studies
Limits:
Child, preschool
/
Female
/
Humans
Language:
En
Journal:
Cardiol Young
Journal subject:
ANGIOLOGIA
/
CARDIOLOGIA
/
PEDIATRIA
Year:
2016
Document type:
Article
Affiliation country: