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Imbalance of plasma amino acids, metabolites and lipids in patients with lysinuric protein intolerance (LPI).
Kurko, Johanna; Tringham, Maaria; Tanner, Laura; Näntö-Salonen, Kirsti; Vähä-Mäkilä, Mari; Nygren, Heli; Pöhö, Päivi; Lietzen, Niina; Mattila, Ismo; Olkku, Anu; Hyötyläinen, Tuulia; Oresic, Matej; Simell, Olli; Niinikoski, Harri; Mykkänen, Juha.
Affiliation
  • Kurko J; Department of Medical Biochemistry and Genetics, University of Turku, Kiinamyllynkatu 10, 20520 Turku, Finland. Electronic address: johanna.kurko@utu.fi.
  • Tringham M; Department of Medical Biochemistry and Genetics, University of Turku, Kiinamyllynkatu 10, 20520 Turku, Finland. Electronic address: maaria.tringham@utu.fi.
  • Tanner L; Department of Medical Biochemistry and Genetics, University of Turku, Kiinamyllynkatu 10, 20520 Turku, Finland; Department of Clinical Genetics, Turku University Hospital, Kiinamyllynkatu 4-8, PL 52, 20521 Turku, Finland. Electronic address: laura.tanner@utu.fi.
  • Näntö-Salonen K; Department of Pediatrics, Turku University Hospital and University of Turku, Kiinamyllynkatu 4-8, PL 52, 20521 Turku, Finland. Electronic address: kirsti.nanto-salonen@tyks.fi.
  • Vähä-Mäkilä M; Department of Pediatrics, Turku University Hospital and University of Turku, Kiinamyllynkatu 4-8, PL 52, 20521 Turku, Finland. Electronic address: mari.vaha-makila@utu.fi.
  • Nygren H; VTT Technical Research Centre of Finland, Tietotie 2, P.O. Boxs 1000, Espoo 02044 VTT, Finland. Electronic address: heli.nygren@vtt.fi.
  • Pöhö P; Faculty of Pharmacy, University of Helsinki, Viikinkaari 5 E, P.O. Boxs 56, Helsinki 00014, Finland. Electronic address: paivi.poho@helsinki.fi.
  • Lietzen N; Turku Centre for Biotechnology, University of Turku and Åbo Akademi University, Tykistökatu 6, 20520 Turku, Finland. Electronic address: nlietzen@btk.fi.
  • Mattila I; Steno Diabetes Center A/S, Niels Steensens Vej 2, 2820 Gentofte, Denmark. Electronic address: imat@steno.dk.
  • Olkku A; Eastern Finland Laboratory Centre, Puijonlaaksontie 2, 70210 Kuopio, Finland. Electronic address: anu.olkku@islab.fi.
  • Hyötyläinen T; Steno Diabetes Center A/S, Niels Steensens Vej 2, 2820 Gentofte, Denmark. Electronic address: tuulia.hyotylainen@utu.fi.
  • Oresic M; Steno Diabetes Center A/S, Niels Steensens Vej 2, 2820 Gentofte, Denmark. Electronic address: matej.oresic@utu.fi.
  • Simell O; Department of Pediatrics, Turku University Hospital and University of Turku, Kiinamyllynkatu 4-8, PL 52, 20521 Turku, Finland. Electronic address: olli.simell@utu.fi.
  • Niinikoski H; Department of Pediatrics, Turku University Hospital and University of Turku, Kiinamyllynkatu 4-8, PL 52, 20521 Turku, Finland. Electronic address: harri.niinikoski@tyks.fi.
  • Mykkänen J; Department of Pediatrics, Turku University Hospital and University of Turku, Kiinamyllynkatu 4-8, PL 52, 20521 Turku, Finland; Research Centre of Applied and Preventive Cardiovascular Medicine, University of Turku, Kiinamyllynkatu 10, 20520 Turku, Finland. Electronic address: juha.mykkanen@utu.fi.
Metabolism ; 65(9): 1361-75, 2016 09.
Article in En | MEDLINE | ID: mdl-27506743

Full text: 1 Collection: 01-internacional Database: MEDLINE Main subject: Amino Acid Metabolism, Inborn Errors / Amino Acids / Lipids / Lysine Limits: Adolescent / Adult / Aged / Child / Female / Humans / Male / Middle aged Country/Region as subject: Europa Language: En Journal: Metabolism Year: 2016 Document type: Article Country of publication:

Full text: 1 Collection: 01-internacional Database: MEDLINE Main subject: Amino Acid Metabolism, Inborn Errors / Amino Acids / Lipids / Lysine Limits: Adolescent / Adult / Aged / Child / Female / Humans / Male / Middle aged Country/Region as subject: Europa Language: En Journal: Metabolism Year: 2016 Document type: Article Country of publication: