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Prenatal diagnosis of congenital ventricular aneurysm and diverticulum: Prenatal features and perinatal management.
Morin, Cecile; Ponzio, Alice; Guirgis, Maurice; Benzouid, Cherine; Beyler, Constance; Rosenblatt, Jonathan.
Affiliation
  • Morin C; Fetal Medicine Unit, Hopital Universitaire Robert Debré, APHP, Paris, France.
  • Ponzio A; Fetal Medicine Unit, Hopital Universitaire Robert Debré, APHP, Paris, France.
  • Guirgis M; Pediatric Cardiology Unit, Hopital Universitaire Robert Debré, APHP, Paris, France.
  • Benzouid C; Pediatric Cardiology Unit, Hopital Universitaire Robert Debré, APHP, Paris, France.
  • Beyler C; Pediatric Cardiology Unit, Hopital Universitaire Robert Debré, APHP, Paris, France.
  • Rosenblatt J; Fetal Medicine Unit, Hopital Universitaire Robert Debré, APHP, Paris, France.
Prenat Diagn ; 42(4): 428-434, 2022 04.
Article in En | MEDLINE | ID: mdl-35238062
ABSTRACT
Congenital ventricular diverticulum (VD) and aneurysm are rare cardiac developmental anomalies and their pathophysiology is still unclear. They present as an anomaly of the four chambers view, cardiomegaly, arrhythmia, pericardial effusion, or hydrops. They are usually isolated anomalies. Differential diagnosis between diverticulum and aneurysm is challenging during the prenatal period. Management policy is not uniform either conservative or repeated pericardial puncture.

OBJECTIVE:

We wanted to describe prenatal features and post-natal outcomes of fetal cardiac out pouching.

METHODS:

We retrospectively report 6 cases of VD and aneurysm prenatally managed in our fetal medicine unit between 2010 and 2020. All cases were evaluated from the first or second trimester of pregnancy until postnatal follow-up (3 months to 3 years).

RESULTS:

All six cases underwent a monthly ultrasound follow-up with spontaneous regression of pericardial effusion, and normal hemodynamics at birth No pericardial puncture was done and postnatal outcome was favorable in all cases.

CONCLUSION:

Based on our experience and on cases previously published, prenatal counseling should be prudent regarding the final diagnosis. Referral and monthly prenatal ultrasound follow-up, birth in a tertiary center after multidisciplinary evaluation and cardiological evaluation at birth still seem mandatory.
Subject(s)

Full text: 1 Collection: 01-internacional Database: MEDLINE Main subject: Pericardial Effusion / Diverticulum / Heart Defects, Congenital / Aneurysm Type of study: Diagnostic_studies / Observational_studies Limits: Female / Humans / Newborn / Pregnancy Language: En Journal: Prenat Diagn Year: 2022 Document type: Article Affiliation country:

Full text: 1 Collection: 01-internacional Database: MEDLINE Main subject: Pericardial Effusion / Diverticulum / Heart Defects, Congenital / Aneurysm Type of study: Diagnostic_studies / Observational_studies Limits: Female / Humans / Newborn / Pregnancy Language: En Journal: Prenat Diagn Year: 2022 Document type: Article Affiliation country:
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