ANCA-Associated Vasculitis in a Patient with Chronic Thromboembolic Pulmonary Hypertension.
Tokai J Exp Clin Med
; 47(1): 26-30, 2022 Apr 20.
Article
in En
| MEDLINE
| ID: mdl-35383867
ABSTRACT
An 82-year-old woman with a history of chronic thromboembolic pulmonary hypertension (CTEPH) presented with malaise, left facial nerve paralysis and the positive seroconversion of myeloperoxidase (MPO)-antineutrophil cytoplasmic antibody (ANCA). She was diagnosed with ANCA-associated vasculitis (AAV). Administration of corticosteroids significantly improved her symptoms, with a decline in the serum MPOANCA level. Ten months later than the initial presentation, she developed an AAV exacerbation with lung infiltration and pericardial effusion, which improved with high-dose corticosteroid therapy. To date, a limited number of AAV cases concomitant with pulmonary hypertension have been reported. The case report presented herein suggests a potential role for CTEPH in the development of AAV.
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Collection:
01-internacional
Database:
MEDLINE
Main subject:
Anti-Neutrophil Cytoplasmic Antibody-Associated Vasculitis
/
Hypertension, Pulmonary
Type of study:
Etiology_studies
/
Risk_factors_studies
Limits:
Aged80
/
Female
/
Humans
Language:
En
Journal:
Tokai J Exp Clin Med
Year:
2022
Document type:
Article