The liver: another organ involved in Muir Torre syndrome?
Fam Cancer
; 11(1): 7-12, 2012 Mar.
Article
in En
| MEDLINE
| ID: mdl-21614588
ABSTRACT
Muir Torre syndrome is a rare autosomal dominant cancer-predisposing syndrome characterized by the occurrence of sebaceous gland neoplasms and/or keratoacanthomas associated with visceral malignancies that belong to the spectrum of hereditary non polyposis colorectal cancer (HNPCC), i.e., tumors of gastrointestinal and genitourinary tracts. Hepatobiliary malignancy in association with Muir Torre syndrome has rarely been reported. Here, we describe a case of Muir Torre syndrome associated with an hepatocellular-carcinoma in a patient with a non-cirrhotic liver and an HNPCC-family with multiple cases of hepatocellular carcinoma.
Full text:
1
Collection:
01-internacional
Database:
MEDLINE
Main subject:
Skin Neoplasms
/
Carcinoma, Hepatocellular
/
Muir-Torre Syndrome
/
Liver Neoplasms
/
Neoplasms, Multiple Primary
Type of study:
Prognostic_studies
Limits:
Adult
/
Aged
/
Aged80
/
Female
/
Humans
/
Male
/
Middle aged
Language:
En
Journal:
Fam Cancer
Journal subject:
NEOPLASIAS
Year:
2012
Document type:
Article
Affiliation country:
Italia