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VCP is essential for mitochondrial quality control by PINK1/Parkin and this function is impaired by VCP mutations.
Neuron ; 78(1): 65-80, 2013 Apr 10.
Article in En | MEDLINE | ID: mdl-23498974
Subject(s)
Adenosine Triphosphatases/metabolism; Cell Cycle Proteins/metabolism; Drosophila Proteins/metabolism; Mitochondria/genetics; Neurons/metabolism; Protein Serine-Threonine Kinases/metabolism; Ubiquitin-Protein Ligases/metabolism; Adaptor Proteins, Vesicular Transport; Adenosine Triphosphatases/genetics; Animals; Animals, Genetically Modified; Carbonyl Cyanide m-Chlorophenyl Hydrazone/pharmacology; Cell Cycle Proteins/genetics; Cells, Cultured; Drosophila; Drosophila Proteins/genetics; Embryo, Mammalian; Enzyme Inhibitors/pharmacology; GTP Phosphohydrolases/metabolism; Ganglia, Spinal/cytology; Gene Expression Regulation/genetics; HSP72 Heat-Shock Proteins/genetics; Humans; Immunoprecipitation; In Vitro Techniques; Intracellular Signaling Peptides and Proteins; Leupeptins/pharmacology; Luminescent Proteins/genetics; Luminescent Proteins/metabolism; Microscopy, Electron, Transmission; Mitochondria/drug effects; Mitochondria/metabolism; Mitochondria/ultrastructure; Mitochondrial Membrane Transport Proteins/metabolism; Mutation/genetics; Neuromuscular Junction/genetics; Neuromuscular Junction/metabolism; Neurons/ultrastructure; Nuclear Proteins/metabolism; Protein Serine-Threonine Kinases/genetics; Protein Tyrosine Phosphatases/genetics; Proteins/metabolism; Proton Ionophores/pharmacology; RNA, Small Interfering/metabolism; RNA, Small Interfering/pharmacology; Time Factors; Transcription Factors/genetics; Transcription Factors/metabolism; Transfection; Ubiquitin-Protein Ligases/genetics; Ubiquitination/genetics; Valosin Containing Protein

Full text: 1 Collection: 01-internacional Database: MEDLINE Main subject: Protein Serine-Threonine Kinases / Adenosine Triphosphatases / Cell Cycle Proteins / Drosophila Proteins / Ubiquitin-Protein Ligases / Mitochondria / Neurons Type of study: Prognostic_studies Language: En Journal: Neuron Journal subject: NEUROLOGIA Year: 2013 Document type: Article Affiliation country: Estados Unidos Country of publication: Estados Unidos

Full text: 1 Collection: 01-internacional Database: MEDLINE Main subject: Protein Serine-Threonine Kinases / Adenosine Triphosphatases / Cell Cycle Proteins / Drosophila Proteins / Ubiquitin-Protein Ligases / Mitochondria / Neurons Type of study: Prognostic_studies Language: En Journal: Neuron Journal subject: NEUROLOGIA Year: 2013 Document type: Article Affiliation country: Estados Unidos Country of publication: Estados Unidos