The prevalence of bronchiectasis in patients with Marfan syndrome.
Int J Tuberc Lung Dis
; 18(8): 995-7, 2014 Aug.
Article
in En
| MEDLINE
| ID: mdl-25199019
ABSTRACT
An association has been suggested between Marfan syndrome (MFS) and the nodular bronchiectatic form of lung disease caused by non-tuberculous mycobacteria (NTM). We evaluated the prevalence of bronchiectasis in 79 adult patients with MFS using computed tomography (CT) imaging. Airway dilation indicative of bronchiectasis (22/79, 28%) and bronchioloectasis (10/79, 13%) were relatively common, although the extent of dilation was not severe and was frequently confined to a single lobe. However, bronchiolitis was evident in only three patients (4%), and no patient was diagnosed with NTM lung disease.
Full text:
1
Collection:
01-internacional
Database:
MEDLINE
Main subject:
Bronchiectasis
/
Marfan Syndrome
/
Nontuberculous Mycobacteria
/
Mycobacterium Infections, Nontuberculous
Type of study:
Observational_studies
/
Prevalence_studies
/
Risk_factors_studies
Limits:
Adult
/
Female
/
Humans
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Male
/
Middle aged
Language:
En
Journal:
Int J Tuberc Lung Dis
Year:
2014
Document type:
Article