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Mapping interactions between complement C3 and regulators using mutations in atypical hemolytic uremic syndrome.
Schramm, Elizabeth C; Roumenina, Lubka T; Rybkine, Tania; Chauvet, Sophie; Vieira-Martins, Paula; Hue, Christophe; Maga, Tara; Valoti, Elisabetta; Wilson, Valerie; Jokiranta, Sakari; Smith, Richard J H; Noris, Marina; Goodship, Tim; Atkinson, John P; Fremeaux-Bacchi, Veronique.
Affiliation
  • Schramm EC; Division of Rheumatology, Department of Medicine, Washington University School of Medicine, Saint Louis, MO;
  • Roumenina LT; INSERM UMRS 1138, Cordeliers Research Center, Paris, France; Université Paris Descartes Sorbonne Paris-Cité, Paris, France; Université Pierre et Marie Curie, Paris, France;
  • Rybkine T; INSERM UMRS 1138, Cordeliers Research Center, Paris, France; Université Paris Descartes Sorbonne Paris-Cité, Paris, France; Université Pierre et Marie Curie, Paris, France;
  • Chauvet S; INSERM UMRS 1138, Cordeliers Research Center, Paris, France; Université Paris Descartes Sorbonne Paris-Cité, Paris, France; Université Pierre et Marie Curie, Paris, France;
  • Vieira-Martins P; INSERM UMRS 1138, Cordeliers Research Center, Paris, France;
  • Hue C; INSERM UMRS 1138, Cordeliers Research Center, Paris, France; Université Paris Descartes Sorbonne Paris-Cité, Paris, France; Université Pierre et Marie Curie, Paris, France;
  • Maga T; Molecular Otolaryngology and Renal Research Laboratories, and Rare Renal Disease Clinic, Departments of Pediatrics and Internal Medicine, Carver College of Medicine, University of Iowa, Iowa City, IA;
  • Valoti E; Laboratory of Immunology and Genetics of Transplantation and Rare Diseases, Mario Negri Institute for Pharmacological Research, Ranica Bergamo, Italy;
  • Wilson V; Northern Molecular Genetics Service, Newcastle upon Tyne Hospitals NHS Foundation Trust, Newcastle upon Tyne, United Kingdom;
  • Jokiranta S; Department of Bacteriology and Immunology, Medicum, and Research Programs Unit, Immunobiology, University of Helsinki and Helsinki University Hospital, Helsinki, Finland;
  • Smith RJ; Molecular Otolaryngology and Renal Research Laboratories, and Rare Renal Disease Clinic, Departments of Pediatrics and Internal Medicine, Carver College of Medicine, University of Iowa, Iowa City, IA;
  • Noris M; Laboratory of Immunology and Genetics of Transplantation and Rare Diseases, Mario Negri Institute for Pharmacological Research, Ranica Bergamo, Italy;
  • Goodship T; Institute of Genetic Medicine, Newcastle University, Newcastle upon Tyne, United Kingdom; and.
  • Atkinson JP; Division of Rheumatology, Department of Medicine, Washington University School of Medicine, Saint Louis, MO;
  • Fremeaux-Bacchi V; INSERM UMRS 1138, Cordeliers Research Center, Paris, France; Université Paris Descartes Sorbonne Paris-Cité, Paris, France; Université Pierre et Marie Curie, Paris, France; Assistance Publique-Hôpitaux de Paris, Service d'Immunologie Biologique, Hôpital Européen Georges Pompidou, Paris, France.
Blood ; 125(15): 2359-69, 2015 Apr 09.
Article in En | MEDLINE | ID: mdl-25608561

Full text: 1 Collection: 01-internacional Database: MEDLINE Main subject: Complement C3 / Protein Interaction Maps / Atypical Hemolytic Uremic Syndrome Type of study: Etiology_studies / Incidence_studies / Observational_studies / Prognostic_studies / Risk_factors_studies Limits: Female / Humans / Male Language: En Journal: Blood Year: 2015 Document type: Article

Full text: 1 Collection: 01-internacional Database: MEDLINE Main subject: Complement C3 / Protein Interaction Maps / Atypical Hemolytic Uremic Syndrome Type of study: Etiology_studies / Incidence_studies / Observational_studies / Prognostic_studies / Risk_factors_studies Limits: Female / Humans / Male Language: En Journal: Blood Year: 2015 Document type: Article