Juvenile dermatomyositis forty years on: Case report.
Neuromuscul Disord
; 28(9): 791-797, 2018 09.
Article
in En
| MEDLINE
| ID: mdl-30064892
ABSTRACT
We present a case report of a 42 year old female, diagnosed at the age of 3 with Juvenile Dermatomyositis. The clinical course was severe and refractory to immunosuppressive therapy. Currently, she is mostly affected by severe muscle atrophy, large joint contractures, calcinosis, and a lipodystrophy associated metabolic syndrome with hypertriglyceridemia, insulin resistance, high total testosterone and hepatic steatosis. She developed Hodgkin´s lymphoma in the course of her disease. Personalized therapeutic choices are discussed as regards juvenile dermatomyositis complications.
Key words
Full text:
1
Collection:
01-internacional
Database:
MEDLINE
Main subject:
Calcinosis
/
Muscular Atrophy
/
Metabolic Syndrome
/
Dermatomyositis
/
Lipodystrophy
Limits:
Adult
/
Child, preschool
/
Female
/
Humans
Language:
En
Journal:
Neuromuscul Disord
Journal subject:
NEUROLOGIA
Year:
2018
Document type:
Article