Use of waxy maize heat modified starch in the treatment of children between 2 and 5â¯years with glycogen storage disease type I: A retrospective study.

Hijazi, Ghada; Pai, Nisha; Nagy, Laura L; Herd, Sarah; Dickson, Jolynn; Ram, Maya; Inbar-Feigenberg, Michal

Use of waxy maize heat modified starch in the treatment of children between 2 and 5â¯years with glycogen storage disease type I: A retrospective study.

Hijazi, Ghada; Pai, Nisha; Nagy, Laura L; Herd, Sarah; Dickson, Jolynn; Ram, Maya; Inbar-Feigenberg, Michal.

Affiliation

Hijazi G; Division of Clinical and Metabolic Genetics, The Hospital for Sick Children, University of Toronto, Toronto, ON, Canada.
Pai N; Division of Clinical and Metabolic Genetics, the Department of Clinical Dietetics, The Hospital for Sick Children, Toronto, ON, Canada.
Nagy LL; Division of Clinical and Metabolic Genetics, the Department of Clinical Dietetics, The Hospital for Sick Children, Toronto, ON, Canada.
Herd S; Division of Clinical and Metabolic Genetics, the Department of Clinical Dietetics, The Hospital for Sick Children, Toronto, ON, Canada.
Dickson J; Division of Clinical and Metabolic Genetics, the Department of Clinical Dietetics, The Hospital for Sick Children, Toronto, ON, Canada.
Ram M; Division of Clinical and Metabolic Genetics, the Department of Clinical Dietetics, The Hospital for Sick Children, Toronto, ON, Canada.
Inbar-Feigenberg M; Division of Clinical and Metabolic Genetics, The Hospital for Sick Children, University of Toronto, Toronto, ON, Canada.

Mol Genet Metab Rep ; 21: 100536, 2019 Dec.

Article in En | MEDLINE | ID: mdl-31844626

Key words

ALT, alanine aminotransferase; AST, aspartate aminotransferase; BMI, body mass index; CNPF, continuous nocturnal pump feed; Continuous nocturnal pump feed (CNPF).; GI, gastrointestinal; GSD, Glycogen storage disease; Glycogen storage disease (GSD); TGs, triglycerides; UCCS, uncooked cornstarch; Uncooked cornstarch (UCCS); WMHMS, waxy maize heat modified starch; Waxy maize heat modified starch (WMHMS); abdominal US, abdominal ultrasound; cm, centimeter; hrs, hours; kg, kilogram

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Full text: 1 Collection: 01-internacional Database: MEDLINE Type of study: Clinical_trials / Observational_studies Language: En Journal: Mol Genet Metab Rep Year: 2019 Document type: Article Affiliation country: Canadá Country of publication: Estados Unidos

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