Dermolytic (dystrophic) epidermolysis bullosa inversa.
Arch Dermatol
; 124(4): 544-7, 1988 Apr.
Article
in En
| MEDLINE
| ID: mdl-3355197
ABSTRACT
We treated four patients with an inverse form of recessive dermolytic (dystrophic) epidermolysis bullosa. The distinguishing features of the disease are (1) early generalized skin involvement with blisters and erosions that heal with superficial, atrophic scars; (2) persistence into adulthood, although milder; (3) severity in flexural areas, especially the inguinal folds, perineum, axillae, submammary area, posterior and lateral aspects of the neck, and often the lower parts of the abdomen and back; (4) normal stature and general development; (5) severe oral and esophageal mucosal involvement; (6) normal teeth; (7) normal or minimally involved fingernails, but mild to moderately dystrophic or atrophic toenail changes; and (8) microscopic findings similar to those of the Hallopeau-Siemens form of epidermolysis bullosa.
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Collection:
01-internacional
Database:
MEDLINE
Main subject:
Epidermolysis Bullosa
Type of study:
Etiology_studies
Limits:
Adult
/
Female
/
Humans
/
Male
Language:
En
Journal:
Arch Dermatol
Year:
1988
Document type:
Article