Pathophysiology and Pathogenesis of Marfan Syndrome.

Zeigler, Sanford M; Sloan, Brandon; Jones, Jeffrey A

Zeigler, Sanford M; Sloan, Brandon; Jones, Jeffrey A.

Affiliation

Zeigler SM; Division of Cardiothoracic Surgery, Department of Surgery, Medical University of South Carolina, Charleston, SC, USA.
Sloan B; Division of Cardiothoracic Surgery, Department of Surgery, Medical University of South Carolina, Charleston, SC, USA.
Jones JA; Division of Cardiothoracic Surgery, Medical University of South Carolina and Ralph H. Johnson Veterans Affairs Medical Center, Charleston, SC, USA. jonesja@musc.edu.

Adv Exp Med Biol ; 1348: 185-206, 2021.

Article in En | MEDLINE | ID: mdl-34807420

Subject(s)
Key words

Aneurysm; Angiotensin receptor blockers (ARBs); Aorta; Collagen; Endoglin; Extracellular matrix; Extracellular signal related kinase (ERK); Fbn1C1039G/+; Fibrillin; Genetic testing; Ghent nosology; Loeys-Dietz syndrome (LDS); Losartan; Marfan syndrome (MFS); Metalloproteinase; Mitogen-activated protein kinase (MAPK); Mitral valve; SMAD; TGF-ß receptor; Thoracic aortic aneurysm and dissection syndrome; Transforming growth factor-ß (TGF-ß); mgR/mgR; ß-Blockers

Fulltext

Add to My VHL

XML

PubMed Links

Search on Google

Full text: 1 Collection: 01-internacional Database: MEDLINE Main subject: Aortic Dissection / Marfan Syndrome Type of study: Diagnostic_studies / Etiology_studies / Prognostic_studies Limits: Humans Language: En Journal: Adv Exp Med Biol Year: 2021 Document type: Article Affiliation country: Estados Unidos

Fulltext

Add to My VHL

XML

PubMed Links

Search on Google