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Loss of endothelial CFTR drives barrier failure and edema formation in lung infection and can be targeted by CFTR potentiation.
Erfinanda, Lasti; Zou, Lin; Gutbier, Birgitt; Kneller, Laura; Weidenfeld, Sarah; Michalick, Laura; Lei, Disi; Reppe, Katrin; Teixeira Alves, Luiz Gustavo; Schneider, Bill; Zhang, Qi; Li, Caihong; Fatykhova, Diana; Schneider, Paul; Liedtke, Wolfgang; Sohara, Eisei; Mitchell, Timothy J; Gruber, Achim D; Hocke, Andreas; Hippenstiel, Stefan; Suttorp, Norbert; Olschewski, Andrea; Mall, Marcus A; Witzenrath, Martin; Kuebler, Wolfgang M.
Affiliation
  • Erfinanda L; Institute of Physiology, Charité-Universitätsmedizin Berlin, 10117 Berlin, Germany.
  • Zou L; Institute of Physiology, Charité-Universitätsmedizin Berlin, 10117 Berlin, Germany.
  • Gutbier B; German Heart Center, 13353 Berlin, Germany.
  • Kneller L; Department of Endocrinology, Shanghai Pudong New Area Gongli Hospital, 200135 Shanghai, China.
  • Weidenfeld S; Department of Infectious Diseases and Pulmonary Medicine, Charité - Universitätsmedizin Berlin, corporate member of Freie Universität Berlin, Humboldt-Universität zu Berlin, and Berlin Institute of Health, 10117 Berlin, Germany.
  • Michalick L; Department of Infectious Diseases and Pulmonary Medicine, Charité - Universitätsmedizin Berlin, corporate member of Freie Universität Berlin, Humboldt-Universität zu Berlin, and Berlin Institute of Health, 10117 Berlin, Germany.
  • Lei D; Institute of Physiology, Charité-Universitätsmedizin Berlin, 10117 Berlin, Germany.
  • Reppe K; Institute of Physiology, Charité-Universitätsmedizin Berlin, 10117 Berlin, Germany.
  • Teixeira Alves LG; Institute of Physiology, Charité-Universitätsmedizin Berlin, 10117 Berlin, Germany.
  • Schneider B; German Heart Center, 13353 Berlin, Germany.
  • Zhang Q; Department of Infectious Diseases and Pulmonary Medicine, Charité - Universitätsmedizin Berlin, corporate member of Freie Universität Berlin, Humboldt-Universität zu Berlin, and Berlin Institute of Health, 10117 Berlin, Germany.
  • Li C; Department of Infectious Diseases and Pulmonary Medicine, Charité - Universitätsmedizin Berlin, corporate member of Freie Universität Berlin, Humboldt-Universität zu Berlin, and Berlin Institute of Health, 10117 Berlin, Germany.
  • Fatykhova D; Department of Infectious Diseases and Pulmonary Medicine, Charité - Universitätsmedizin Berlin, corporate member of Freie Universität Berlin, Humboldt-Universität zu Berlin, and Berlin Institute of Health, 10117 Berlin, Germany.
  • Schneider P; Institute of Physiology, Charité-Universitätsmedizin Berlin, 10117 Berlin, Germany.
  • Liedtke W; Institute of Physiology, Charité-Universitätsmedizin Berlin, 10117 Berlin, Germany.
  • Sohara E; Department of Infectious Diseases and Pulmonary Medicine, Charité - Universitätsmedizin Berlin, corporate member of Freie Universität Berlin, Humboldt-Universität zu Berlin, and Berlin Institute of Health, 10117 Berlin, Germany.
  • Mitchell TJ; Department for General and Thoracic Surgery, DRK Clinics, 13359 Berlin, Germany.
  • Gruber AD; Departments of Neurology, Neurobiology, and Clinics for Pain and Palliative Care, Duke University Medical Center, Durham, NC 27710, USA.
  • Hocke A; Department of Nephrology, Graduate School of Medical and Dental Sciences, Tokyo Medical and Dental University, Tokyo 113-8510, Japan.
  • Hippenstiel S; Institute of Microbiology and Infection, University of Birmingham, Birmingham B15-2TT, UK.
  • Suttorp N; Institute of Veterinary Pathology, Freie Universität Berlin, 14163 Berlin, Germany.
  • Olschewski A; Department of Infectious Diseases and Pulmonary Medicine, Charité - Universitätsmedizin Berlin, corporate member of Freie Universität Berlin, Humboldt-Universität zu Berlin, and Berlin Institute of Health, 10117 Berlin, Germany.
  • Mall MA; German Center for Lung Research (DZL), associated partner site, 10117 Berlin, Germany.
  • Witzenrath M; Department of Infectious Diseases and Pulmonary Medicine, Charité - Universitätsmedizin Berlin, corporate member of Freie Universität Berlin, Humboldt-Universität zu Berlin, and Berlin Institute of Health, 10117 Berlin, Germany.
  • Kuebler WM; German Center for Lung Research (DZL), associated partner site, 10117 Berlin, Germany.
Sci Transl Med ; 14(674): eabg8577, 2022 12 07.
Article in En | MEDLINE | ID: mdl-36475904

Full text: 1 Collection: 01-internacional Database: MEDLINE Main subject: Pneumonia / Chlorides Type of study: Prognostic_studies Limits: Animals / Humans Language: En Journal: Sci Transl Med Journal subject: CIENCIA / MEDICINA Year: 2022 Document type: Article Affiliation country: Alemania Country of publication: Estados Unidos

Full text: 1 Collection: 01-internacional Database: MEDLINE Main subject: Pneumonia / Chlorides Type of study: Prognostic_studies Limits: Animals / Humans Language: En Journal: Sci Transl Med Journal subject: CIENCIA / MEDICINA Year: 2022 Document type: Article Affiliation country: Alemania Country of publication: Estados Unidos