Autosomal Recessive Polycystic Kidney Disease: Diagnosis, Prognosis, and Management.
Adv Kidney Dis Health
; 30(5): 468-476, 2023 09.
Article
in En
| MEDLINE
| ID: mdl-38097335
ABSTRACT
Autosomal recessive polycystic kidney disease (ARPKD) is the rare and usually early-onset form of polycystic kidney disease with a typical clinical presentation of enlarged cystic kidneys and liver involvement with congenital hepatic fibrosis or Caroli syndrome. ARPKD remains a clinical challenge in pediatrics, frequently requiring continuous and long-term multidisciplinary treatment. In this review, we aim to give an overview over clinical aspects of ARPKD and recent developments in our understanding of disease progression, risk patterns, and treatment of ARPKD.
Key words
Full text:
1
Collection:
01-internacional
Database:
MEDLINE
Main subject:
Polycystic Kidney, Autosomal Recessive
/
Caroli Disease
Limits:
Child
/
Humans
Language:
En
Journal:
Adv Kidney Dis Health
Year:
2023
Document type:
Article
Affiliation country:
Alemania