Congenital Langerhans Cell Histiocytosis With the Skin and Lung Involvement: A Case and Literature Review.
Cureus
; 15(11): e49453, 2023 Nov.
Article
in En
| MEDLINE
| ID: mdl-38152801
ABSTRACT
Langerhans cell histiocytosis (LCH) is a clonal proliferative disease of immature Langerhans cells that expand in various organs, leading to organ and tissue dysfunction. Although LCH is most commonly seen in children under the age of three, a small number of cases of congenital LCH have been described. With a review of the literature on congenital LCH with lung and skin lesions, we present a case of congenital LCH with involvement of skin and lung, which was effectively treated with chemotherapy without recurrence for 3 years during the observational period. In addition, we summarized previously published case studies of congenital LCH with skin and lung involvement.
Full text:
1
Collection:
01-internacional
Database:
MEDLINE
Language:
En
Journal:
Cureus
Year:
2023
Document type:
Article
Country of publication:
Estados Unidos