Autosomal Dominant Polycystic Kidney Disease with an Asymptomatic Type I Choledochal Cyst / 대한내과학회지
Korean Journal of Medicine
; : 205-209, 2013.
Article
in Ko
| WPRIM
| ID: wpr-70552
Responsible library:
WPRO
ABSTRACT
Autosomal dominant polycystic kidney disease (ADPKD) is the most common inherited renal disease. Polycystic liver disease is commonly observed in ADPKD but rarely has it been associated with a choledochal cyst. We report a case of a choledochal cyst with ADPKD in a 60-year-old female patient with ADPKD and concomitant chronic renal failure who was admitted because of acute deterioration of kidney function due to poor oral intake. There was no history of a biliary disorder and her kidney function recovered promptly after fluid replacement. Non-enhanced computed tomography was performed to evaluate ADPKD and revealed numerous cysts in both kidneys and liver. It also showed fusiform dilatation of the extrahepatic bile ducts, a finding indicative of a choledochal cyst. Liver function was within the normal range and there was no evidence of extrahepatic biliary obstruction. Magnetic resonance cholangiopancreatography confirmed the diagnosis of a type I choledochal cyst combined with ADPKD.
Key words
Full text:
1
Database:
WPRIM
Main subject:
Reference Values
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Choledochal Cyst
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Polycystic Kidney, Autosomal Dominant
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Bile Ducts, Extrahepatic
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Cysts
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Cholangiopancreatography, Magnetic Resonance
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Dilatation
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Kidney
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Kidney Failure, Chronic
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Liver
Limits:
Female
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Humans
Language:
Ko
Journal:
Korean Journal of Medicine
Year:
2013
Document type:
Article