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Vasculopatía Livedoide, la punta del témpano: a propósito de un caso / Livedoid vasculopathy, the tip of the iceberg: a case report
Brusa, JR; Andrade, MN; Gallmann, AL; Rossello, VE; Gomez Zanni, MS; Guidi, A; Papa, MB.
Affiliation
  • Brusa, JR; Universitaria. Ciudad de Córdoba.
  • Andrade, MN; Universitaria. Ciudad de Córdoba.
  • Gallmann, AL; Universitaria. Ciudad de Córdoba.
  • Rossello, VE; Universitaria. Ciudad de Córdoba.
  • Gomez Zanni, MS; Universitaria. Ciudad de Córdoba.
  • Guidi, A; Universitaria. Ciudad de Córdoba.
  • Papa, MB; Universitaria. Ciudad de Córdoba.
Rev. argent. dermatol ; 102(2): 1-10, jun. 2021. graf
Article in Spanish | LILACS-Express | LILACS | ID: biblio-1356967
Responsible library: AR1.1
RESUMEN
Resumen La vasculopatía livedoide (VL), es una enfermedad vascular oclusiva que afecta la microvasculatura, se caracteriza por ser recurrente y no inflamatoria. Su incidencia es de 1/100.000 casos por habitantes, afectando en su mayoría a mujeres de edad media. Su patogenia se desconoce, pero se destaca el componente trombótico de la misma, causado por un estado de hipercoagulabilidad, que conduce a la oclusión vascular, debiendo distinguirse una forma primaria y una secundaria.Clínicamente se observan úlceras dolorosas a nivel maleolar que evolucionan progresivamente a una cicatrización atrófica, blanquecina nacarada y estrellada característica.Presentamos un caso clínico en un varón con múltiples comorbilidades y difícil tratamiento, el cual requirió un trabajo multidisciplinario.
ABSTRACT
Abstract Livedoid vascular disease (VL), is an occlusive vascular disease that affects the microvasculature, is characterized by being recurrent and non-inflammatory. Its incidence is 1 / 100,000 cases per inhabitant, affecting mostly middle-aged women. Its pathogenesis is unknown, but its thrombotic component stands out, caused by a state of hypercoagulability, which leads to vascular occlusion, and a primary and secondary form must be distinguished. Clinically, painful ulcers are observed at the malleolar level, progressing progressively to characteristic atrophic, pearly whitish and starry healing. We present a clinical case in a male with multiple comorbidities and difficult management, which required multidisciplinary work.

Full text: Available Collection: International databases Database: LILACS Language: Spanish Journal: Rev. argent. dermatol Journal subject: Dermatology Year: 2021 Document type: Article
Full text: Available Collection: International databases Database: LILACS Language: Spanish Journal: Rev. argent. dermatol Journal subject: Dermatology Year: 2021 Document type: Article
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