Amiloidosis cardiaca senil y estenosis aórtica degenerativa: 2 enfermedades interrelacionadas en el anciano / Wild-type transthyretin-related cardiac amyloidosis and degenerative aortic stenosis: two inter-related pathologies in the elderly
Rev. esp. geriatr. gerontol. (Ed. impr.)
; 52(3): 167-170, mayo-jun. 2017. ilus
Article
in Es
| IBECS
| ID: ibc-162846
Responsible library:
ES1.1
Localization: BNCS
RESUMEN
La variedad senil de la amiloidosis por transtiretina (ATTRwt) presenta algunas características clínicas que se superponen con las de la estenosis aórtica (EA) degenerativa. Recientemente se ha planteado la posibilidad de que algunas de las complicaciones que pueden tener lugar durante y tras el implante percutáneo de prótesis valvular aórtica (TAVI), puedan deberse a una ATTRwt coexistente, puesto que se ha encontrado amiloidosis hasta en un tercio de las autopsias de pacientes sometidos a implante de TAVI. A continuación describimos 2 casos de ATTRwt en pacientes con EA que iban dirigidos a implante de TAVI. Dado que se ha visto que la ATTRwt tiene un curso clínico lento, habría que replantear las decisiones sobre la actitud terapéutica en estos pacientes (AU)
ABSTRACT
Wild-type transthyretin-related cardiac amyloidosis (ATTRwt) and degenerative aortic stenosis share a common demographic and clinical profile. It was recently suggested that some of the complications arising during and after transcatheter aortic valve replacement (TAVR) could be due to a co-existing cardiac amyloidosis. In a series of autopsies of patients who had undergone TAVR, researchers found ATTR amyloidosis in one third of the cases. A report is presented on two patients with aortic stenosis who were diagnosed with ATTRwt when they were about to undergo a TAVI. ATTRwt is a slowly progressing disease so we need to review the decisions on the therapeutic approach in these patients (AU)
Full text:
1
Collection:
06-national
/
ES
Database:
IBECS
Main subject:
Aortic Valve Stenosis
/
Heart Valve Prosthesis
/
Amyloidosis
Type of study:
Prognostic_studies
Limits:
Aged
/
Humans
/
Male
Language:
Es
Journal:
Rev. esp. geriatr. gerontol. (Ed. impr.)
Year:
2017
Document type:
Article