Linfoma intravascular, un desafio diagnóstico: Caso clínico / Intravascular lymphoma: Report of one case
Rev. méd. Chile
; 143(8): 1076-1080, ago. 2015. ilus
Article
in Es
| LILACS
| ID: lil-762674
Responsible library:
CL1.1
ABSTRACT
Intravascular lymphoma is a rare subtype of extranodal diffuse large B-cell lymphoma characterized by clonal proliferation of lymphocytes inside of small and medium caliber vessels. Its incidence is estimated at one case per million. The clinical picture is very variable, but frequently has skin and central nervous system involvement. It is diagnosed by demonstrating pathological blood vessel infiltration by lymphoma cells. We report a 44 years old male presenting with fever, malaise and erythematous lesions in the abdominal wall. An abdominal wall biopsy showed dilated vascular vessels with atypical cells in their lumen, compatible with large B-cell intravascular lymphoma. He was treated with rituximab, cyclophosphamide, adriamycin, vincristine and prednisone and an autologous hematopoietic stem cell transplantation, achieving a complete remission that has lasted two years.
Key words
Full text:
1
Collection:
01-internacional
Database:
LILACS
Main subject:
Lymphoma, Large B-Cell, Diffuse
/
Vascular Neoplasms
Type of study:
Diagnostic_studies
Limits:
Adult
/
Humans
/
Male
Language:
Es
Journal:
Rev. méd. Chile
Journal subject:
MEDICINA
Year:
2015
Document type:
Article
Affiliation country:
Argentina
Country of publication:
Chile