Immune-deficient bronchiectasis associated with X-linked lymphoproliferative disease.
Ann Thorac Surg
; 68(2): 578-80, 1999 Aug.
Article
in En
| MEDLINE
| ID: mdl-10475441
ABSTRACT
Bronchiectasis may occur with various congenital and acquired immunodeficiency diseases. The association of bronchiectasis and the X-linked lymphoproliferative disease (XLP), also known as Duncan's disease is unknown. We describe the case of a 39-year-old man with XLP, the oldest surviving, who developed chronic bronchiectasis with hemoptysis and required a pneumonectomy to control his symptoms.
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Collection:
01-internacional
Database:
MEDLINE
Main subject:
Bronchiectasis
/
Lymphoproliferative Disorders
Type of study:
Risk_factors_studies
Limits:
Adult
/
Humans
/
Male
Language:
En
Journal:
Ann Thorac Surg
Year:
1999
Document type:
Article
Affiliation country:
United States