[Anesthetic management of a child with congenital sensory neuropathy with anhydrosis].
Masui
; 50(7): 789-91, 2001 Jul.
Article
in Ja
| MEDLINE
| ID: mdl-11510075
ABSTRACT
Congenital sensory neuropathy with anhydrosis is a rare disorder characterized by insensitivity to pain with normal tactile perception, self-mutilation, anhydrosis, recurrent unexplained fever, mental retardation and variable autonomic abnormality. We managed a 14-year-old boy with this syndrome who underwent repair of right femur fracture. Anesthesia was induced with propofol and ketamine. Adequate depth of anesthesia was carefully controlled by processed electroencephalogram, and core body temperature was maintained at 37.0 degrees C during the surgery. The patient was well sedated, and nausea and vomiting were not noted postoperatively. Use of droperidol and propofol may be beneficial for anesthetic management of this syndrome, because droperidol exerts residual hypnotic effect postoperatively, and both drugs have antiemetic property.
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Collection:
01-internacional
Database:
MEDLINE
Main subject:
Hereditary Sensory and Autonomic Neuropathies
/
Anesthesia, Intravenous
Limits:
Adolescent
/
Humans
/
Male
Language:
Ja
Journal:
Masui
Year:
2001
Document type:
Article