Tyrosinemia I, a model for human diseases mediated by 2-oxoacid-utilizing dioxygenases: hepatotoxin suppression by NTBC does not normalize hepatic collagen metabolism.

Hanauske-Abel, Hartmut M; Popowicz, Anthony; Remotti, Helen; Newfield, Ron S; Levy, Joseph

Hanauske-Abel, Hartmut M; Popowicz, Anthony; Remotti, Helen; Newfield, Ron S; Levy, Joseph.

Affiliation

Hanauske-Abel HM; Departments of Pediatrics and Pathology, New York-Presbyterian Hospital, Columbia and Cornell Campuses, Rockefeller University, New York, New York, USA. hmhanauske@earthlink.net

J Pediatr Gastroenterol Nutr ; 35(1): 73-8, 2002 Jul.

Article in En | MEDLINE | ID: mdl-12142814

Subject(s)

4-Hydroxyphenylpyruvate Dioxygenase/metabolism; Collagen/metabolism; Cyclohexanones/therapeutic use; Liver/metabolism; Nitrobenzoates/therapeutic use; Procollagen-Proline Dioxygenase/metabolism; Tyrosinemias/enzymology; Cyclohexanones/chemistry; Cyclohexanones/metabolism; Enzyme Inhibitors/chemistry; Enzyme Inhibitors/metabolism; Enzyme Inhibitors/therapeutic use; Humans; Infant; Models, Molecular; Molecular Structure; Nitrobenzoates/chemistry; Nitrobenzoates/metabolism; Tyrosinemias/drug therapy; Tyrosinemias/metabolism

Search on Google

Add to My VHL

XML

PubMed Links

Collection: 01-internacional Database: MEDLINE Main subject: Collagen / Procollagen-Proline Dioxygenase / Tyrosinemias / Cyclohexanones / 4-Hydroxyphenylpyruvate Dioxygenase / Liver / Nitrobenzoates Type of study: Prognostic_studies Limits: Humans / Infant Language: En Journal: J Pediatr Gastroenterol Nutr Year: 2002 Document type: Article Affiliation country: United States

Search on Google

Add to My VHL

XML

PubMed Links