Congenital atresia of the portal vein and extrahepatic portocaval shunt associated with benign neonatal hemangiomatosis, congenital adrenal hyperplasia, and atrial septal defect.
J Pediatr Surg
; 38(4): 633-4, 2003 Apr.
Article
in En
| MEDLINE
| ID: mdl-12677584
ABSTRACT
A rare case of congenital atresia of the portal vein and ductus venosus, extrahepatic portocaval shunt, benign neonatal hemangiomatosis, congenital adrenal hyperplasia, and an atrial septal defect is reported. Twenty-two cases of congenital extrahepatic end-to-side shunts have been described before. Although additional anomalies are common in this type of shunt, hemangiomatosis has been described only once. Adrenal hyperplasia has never been reported in this anomaly.
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Collection:
01-internacional
Database:
MEDLINE
Main subject:
Portal Vein
/
Skin Neoplasms
/
Vena Cava, Inferior
/
Abnormalities, Multiple
/
Adrenal Hyperplasia, Congenital
/
Heart Septal Defects, Atrial
/
Hemangioma
/
Neoplasms, Multiple Primary
Type of study:
Etiology_studies
/
Risk_factors_studies
Limits:
Adult
/
Female
/
Humans
/
Newborn
/
Pregnancy
Language:
En
Journal:
J Pediatr Surg
Year:
2003
Document type:
Article
Affiliation country:
Germany