Radiological manifestations of abdominopelvic nerve tumours seen in neurofibromatosis type 1.
Clin Radiol
; 69(4): 431-5, 2014 Apr.
Article
in En
| MEDLINE
| ID: mdl-24361143
Neurofibromatosis type 1 (NF1) is the most common of the phakomatoses, which is inherited in an autosomal dominant pattern. Neurofibromas arise from Schwann cells and fibroblasts and plexiform neurofibromas are pathognomonic for NF1, which may arise in any peripheral nerve. The clinical expression of NF1 is extremely variable and gastrointestinal manifestations of NF1 are relatively uncommon. The purpose of this article is to illustrate the abdominal ultrasound, computed tomography, and magnetic resonance imaging findings of abdominopelvic nerve tumours seen in NF1 in both paediatric and adult patients.
Full text:
1
Collection:
01-internacional
Database:
MEDLINE
Main subject:
Pelvis
/
Peripheral Nerves
/
Magnetic Resonance Imaging
/
Tomography, X-Ray Computed
/
Neurofibromatosis 1
/
Neurofibroma, Plexiform
/
Nerve Sheath Neoplasms
Type of study:
Diagnostic_studies
/
Prognostic_studies
Limits:
Adolescent
/
Adult
/
Child
/
Female
/
Humans
/
Male
Language:
En
Journal:
Clin Radiol
Year:
2014
Document type:
Article
Country of publication:
United kingdom