[Case of ataxic sensory neuronopathy associated with Sjögren's syndrome].
Rinsho Shinkeigaku
; 54(5): 413-6, 2014.
Article
in Ja
| MEDLINE
| ID: mdl-24943078
ABSTRACT
A 71-year-old woman developed advanced thermal hypoalgesia, bathyesthesia, and significant sensory ataxia 1 year ago. She also had difficulty maintaining a sitting posture. Patchy and reduced thermal nociception corresponding to a dermatome was found in her four extremities and trunk. On the basis of several tests, she was diagnosed with ataxic sensory neuronopathy due to dorsal root ganglionitis associated with Sjögren's syndrome. Generally, dorsal root ganglionitis associated with Sjögren's syndrome is refractory. After treatment with simple plasmapheresis, she was able to maintain a sitting posture. Finally, her symptoms stabilized after the inclusion of oral D-penicillamine to her treatment regimen. Although the clinical course was observed for about one year, we report this case because of its valuable finding, i.e., her symptoms improved after simple plasmapheresis and oral administration of D-penicillamine.
Search on Google
Collection:
01-internacional
Database:
MEDLINE
Main subject:
Ataxia
/
Sjogren's Syndrome
/
Ganglia, Spinal
/
Neuritis
Type of study:
Risk_factors_studies
Limits:
Aged
/
Female
/
Humans
Language:
Ja
Journal:
Rinsho Shinkeigaku
Year:
2014
Document type:
Article