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Genetic Inhibition Of The Ubiquitin Ligase Rnf5 Attenuates Phenotypes Associated To F508del Cystic Fibrosis Mutation.
Tomati, Valeria; Sondo, Elvira; Armirotti, Andrea; Caci, Emanuela; Pesce, Emanuela; Marini, Monica; Gianotti, Ambra; Jeon, Young Ju; Cilli, Michele; Pistorio, Angela; Mastracci, Luca; Ravazzolo, Roberto; Scholte, Bob; Ronai, Ze'ev; Galietta, Luis J V; Pedemonte, Nicoletta.
Affiliation
  • Tomati V; Istituto Giannina Gaslini, Genova, Italy.
  • Sondo E; Istituto Giannina Gaslini, Genova, Italy.
  • Armirotti A; Department of Drug Discovery and Development, Istituto Italiano di Tecnologia, Genova, Italy.
  • Caci E; Istituto Giannina Gaslini, Genova, Italy.
  • Pesce E; Istituto Giannina Gaslini, Genova, Italy.
  • Marini M; Istituto Giannina Gaslini, Genova, Italy.
  • Gianotti A; Istituto Giannina Gaslini, Genova, Italy.
  • Jeon YJ; The Burnham Institute for Medical Research, La Jolla, California, USA.
  • Cilli M; IRCCS AOU San Martino-IST, Genova, Italy.
  • Pistorio A; Istituto Giannina Gaslini, Genova, Italy.
  • Mastracci L; 1] IRCCS AOU San Martino-IST, Genova, Italy [2] Anatomic Pathology Unit, Department of Surgical Sciences and Integrated Diagnostics, University of Genova, Italy.
  • Ravazzolo R; 1] Istituto Giannina Gaslini, Genova, Italy [2] DINOGMI Department, University of Genova, Italy.
  • Scholte B; Cell Biology Department, Erasmus Medical Center, Rotterdam, The Netherlands.
  • Ronai Z; The Burnham Institute for Medical Research, La Jolla, California, USA.
  • Galietta LJ; Istituto Giannina Gaslini, Genova, Italy.
  • Pedemonte N; Istituto Giannina Gaslini, Genova, Italy.
Sci Rep ; 5: 12138, 2015 Jul 17.
Article in En | MEDLINE | ID: mdl-26183966

Full text: 1 Collection: 01-internacional Database: MEDLINE Main subject: Phenotype / Sequence Deletion / Cystic Fibrosis Transmembrane Conductance Regulator / Cystic Fibrosis / Ubiquitin-Protein Ligases / DNA-Binding Proteins / Genetic Association Studies Type of study: Risk_factors_studies Limits: Animals / Humans Language: En Journal: Sci Rep Year: 2015 Document type: Article Affiliation country: Italy Country of publication: United kingdom

Full text: 1 Collection: 01-internacional Database: MEDLINE Main subject: Phenotype / Sequence Deletion / Cystic Fibrosis Transmembrane Conductance Regulator / Cystic Fibrosis / Ubiquitin-Protein Ligases / DNA-Binding Proteins / Genetic Association Studies Type of study: Risk_factors_studies Limits: Animals / Humans Language: En Journal: Sci Rep Year: 2015 Document type: Article Affiliation country: Italy Country of publication: United kingdom