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The case of an APDS patient: Defects in maturation and function and decreased in vitro anti-mycobacterial activity in the myeloid compartment.
Chiriaco, Maria; Brigida, Immacolata; Ariganello, Paola; Di Cesare, Silvia; Di Matteo, Gigliola; Taus, Francesco; Cittaro, Davide; Lazarevic, Dejan; Scarselli, Alessia; Santilli, Veronica; Attardi, Enrico; Stupka, Elia; Giannelli, Stefania; Fraziano, Maurizio; Finocchi, Andrea; Rossi, Paolo; Aiuti, Alessandro; Palma, Paolo; Cancrini, Caterina.
Affiliation
  • Chiriaco M; University Department of Pediatrics, Unit of Immune and Infectious Diseases, Childrens' Hospital Bambino Gesù, Rome, Italy; Department of Systems Medicine, University of Rome "Tor Vergata", Rome, Italy.
  • Brigida I; San Raffaele Telethon Institute for Gene Therapy (TIGET), Italy.
  • Ariganello P; University Department of Pediatrics, Unit of Immune and Infectious Diseases, Childrens' Hospital Bambino Gesù, Rome, Italy; Department of Systems Medicine, University of Rome "Tor Vergata", Rome, Italy.
  • Di Cesare S; University Department of Pediatrics, Unit of Immune and Infectious Diseases, Childrens' Hospital Bambino Gesù, Rome, Italy; Department of Systems Medicine, University of Rome "Tor Vergata", Rome, Italy.
  • Di Matteo G; University Department of Pediatrics, Unit of Immune and Infectious Diseases, Childrens' Hospital Bambino Gesù, Rome, Italy; Department of Systems Medicine, University of Rome "Tor Vergata", Rome, Italy.
  • Taus F; Department of Biology, University of Rome "Tor Vergata", Rome, Italy.
  • Cittaro D; Center for Translational Genomics and BioInformatics, San Raffaele Scientific Institute, Milan, Italy.
  • Lazarevic D; Center for Translational Genomics and BioInformatics, San Raffaele Scientific Institute, Milan, Italy.
  • Scarselli A; University Department of Pediatrics, Unit of Immune and Infectious Diseases, Childrens' Hospital Bambino Gesù, Rome, Italy; Department of Systems Medicine, University of Rome "Tor Vergata", Rome, Italy.
  • Santilli V; University Department of Pediatrics, Unit of Immune and Infectious Diseases, Childrens' Hospital Bambino Gesù, Rome, Italy; Department of Systems Medicine, University of Rome "Tor Vergata", Rome, Italy.
  • Attardi E; University Department of Pediatrics, Unit of Immune and Infectious Diseases, Childrens' Hospital Bambino Gesù, Rome, Italy; Department of Systems Medicine, University of Rome "Tor Vergata", Rome, Italy.
  • Stupka E; Center for Translational Genomics and BioInformatics, San Raffaele Scientific Institute, Milan, Italy.
  • Giannelli S; San Raffaele Telethon Institute for Gene Therapy (TIGET), Italy.
  • Fraziano M; Department of Biology, University of Rome "Tor Vergata", Rome, Italy.
  • Finocchi A; University Department of Pediatrics, Unit of Immune and Infectious Diseases, Childrens' Hospital Bambino Gesù, Rome, Italy; Department of Systems Medicine, University of Rome "Tor Vergata", Rome, Italy.
  • Rossi P; University Department of Pediatrics, Unit of Immune and Infectious Diseases, Childrens' Hospital Bambino Gesù, Rome, Italy; Department of Systems Medicine, University of Rome "Tor Vergata", Rome, Italy.
  • Aiuti A; San Raffaele Telethon Institute for Gene Therapy (TIGET), Italy; Pediatric Immunohematology, San Raffaele Scientific Institute, Milan, Italy; Vita-Salute San Raffaele University, Milan, Italy.
  • Palma P; University Department of Pediatrics, Unit of Immune and Infectious Diseases, Childrens' Hospital Bambino Gesù, Rome, Italy; Department of Systems Medicine, University of Rome "Tor Vergata", Rome, Italy.
  • Cancrini C; University Department of Pediatrics, Unit of Immune and Infectious Diseases, Childrens' Hospital Bambino Gesù, Rome, Italy. Electronic address: cancrini@med.uniroma2.it.
Clin Immunol ; 178: 20-28, 2017 05.
Article in En | MEDLINE | ID: mdl-26732860

Full text: 1 Collection: 01-internacional Database: MEDLINE Main subject: Dendritic Cells / B-Lymphocytes / Cell Differentiation / Immunologic Deficiency Syndromes / Macrophages Limits: Adult / Humans / Male Language: En Journal: Clin Immunol Journal subject: ALERGIA E IMUNOLOGIA Year: 2017 Document type: Article Affiliation country: Italy Country of publication: United States

Full text: 1 Collection: 01-internacional Database: MEDLINE Main subject: Dendritic Cells / B-Lymphocytes / Cell Differentiation / Immunologic Deficiency Syndromes / Macrophages Limits: Adult / Humans / Male Language: En Journal: Clin Immunol Journal subject: ALERGIA E IMUNOLOGIA Year: 2017 Document type: Article Affiliation country: Italy Country of publication: United States