Von Meyenburg complex and complete ductal plate malformation along with Klatskin tumour: a rare association.
BMJ Case Rep
; 2016: 10.1136/bcr-2016-215220, 2016 Apr 18.
Article
in En
| MEDLINE
| ID: mdl-27090552
ABSTRACT
Von Meyenburg complexes (VMCs), or bile duct microhamartomas, are among the constellation of defects of ductal plate malformation. These present as multiple small intrahepatic cysts and are diagnosed incidentally. Association of intrahepatic VMCs with a bile duct cancer has rarely been reported. We describe a case of a 53-year-old man presenting with obstructive jaundice. Biochemistry and radiology gave a provisional diagnosis of a resectable Klatskin tumour. The patient underwent right hepatectomy with common bile duct and caudate lobe excision. The histopathological examination demonstrated intrahepatic VMCs with complete ductal malformation and malignancy at the hilum.
Full text:
1
Collection:
01-internacional
Database:
MEDLINE
Main subject:
Bile Duct Diseases
/
Bile Duct Neoplasms
/
Bile Ducts
/
Klatskin Tumor
/
Hamartoma
Type of study:
Risk_factors_studies
Limits:
Humans
/
Male
/
Middle aged
Language:
En
Journal:
BMJ Case Rep
Year:
2016
Document type:
Article
Affiliation country:
India