Cochlear implantation in Pendred syndrome and non-syndromic enlarged vestibular aqueduct - clinical challenges, surgical results, and complications.
Acta Otolaryngol
; 136(10): 1064-8, 2016 Oct.
Article
in En
| MEDLINE
| ID: mdl-27241825
ABSTRACT
OBJECTIVE:
To explore specific clinical issues, surgical results, and complications of 80 cochlear implantations (CI) in 55 patients with Pendred syndrome (PS) or non-syndromic enlarged vestibular aqueduct (NSEVA).BACKGROUND:
Previous studies have focused either on unselected case series or on populations with mixed cochlear malformations. PS/NSEVA accounts for up to 10% of congenital SNHL, rendering this a large group of cochlear implant candidates. The abnormal inner ear anatomy of these patients may be associated with a lower surgical success rate and a higher rate of complications. STUDYDESIGN:
Retrospective review of patients' medical records and CT/MRI.SETTING:
Tertiary referral center. MATERIALS ANDMETHODS:
The medical records and CT/MRI images of 55 PS/NSEVA patients receiving 80 cochlear implantations from 1982-2014 were reviewed. Demographic data, surgical results, intra-operative incidents, and post-operative complications were retrieved.RESULTS:
Complications occurred in 36% of implantations; 5% hereof major complications. Gushing/oozing from the cochleostoma occurred in 10% of implantations and was related to transient, but not prolonged post-operative vertigo.CONCLUSION:
Intra-operative risks of gushing/oozing and post-operative vertigo are the primary clinical issues in PS/NSEVA patients regarding CI. Nonetheless, the surgical success rate is high and the major complication rate is low; similar to studies of unselected series of CI recipients.Key words
Full text:
1
Collection:
01-internacional
Database:
MEDLINE
Main subject:
Vestibular Aqueduct
/
Cochlear Implantation
/
Goiter, Nodular
/
Hearing Loss, Sensorineural
Type of study:
Observational_studies
/
Risk_factors_studies
Limits:
Child
/
Child, preschool
/
Female
/
Humans
/
Infant
/
Male
/
Newborn
Country/Region as subject:
Europa
Language:
En
Journal:
Acta Otolaryngol
Year:
2016
Document type:
Article