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Respiratory chain enzyme deficiency induces mitochondrial location of actin-binding gelsolin to modulate the oligomerization of VDAC complexes and cell survival.
García-Bartolomé, Alberto; Peñas, Ana; Marín-Buera, Lorena; Lobo-Jarne, Teresa; Pérez-Pérez, Rafael; Morán, María; Arenas, Joaquín; Martín, Miguel A; Ugalde, Cristina.
Affiliation
  • García-Bartolomé A; Instituto de Investigación, Hospital Universitario 12 de Octubre, Madrid 28041, Spain.
  • Peñas A; Centro de Investigación Biomédica en Red de Enfermedades Raras (CIBERER), Madrid U723, Spain.
  • Marín-Buera L; Instituto de Investigación, Hospital Universitario 12 de Octubre, Madrid 28041, Spain.
  • Lobo-Jarne T; Instituto de Investigación, Hospital Universitario 12 de Octubre, Madrid 28041, Spain.
  • Pérez-Pérez R; Department of Biochemistry and Biophysics, Center for Biomembrane Research, Stockholm University, SE-106 91 Stockholm, Sweden.
  • Morán M; Instituto de Investigación, Hospital Universitario 12 de Octubre, Madrid 28041, Spain.
  • Arenas J; Centro de Investigación Biomédica en Red de Enfermedades Raras (CIBERER), Madrid U723, Spain.
  • Martín MA; Instituto de Investigación, Hospital Universitario 12 de Octubre, Madrid 28041, Spain.
  • Ugalde C; Centro de Investigación Biomédica en Red de Enfermedades Raras (CIBERER), Madrid U723, Spain.
Hum Mol Genet ; 26(13): 2493-2506, 2017 07 01.
Article in En | MEDLINE | ID: mdl-28431142

Full text: 1 Collection: 01-internacional Database: MEDLINE Main subject: Gelsolin / Electron Transport / Voltage-Dependent Anion Channel 1 Limits: Humans Language: En Journal: Hum Mol Genet Journal subject: BIOLOGIA MOLECULAR / GENETICA MEDICA Year: 2017 Document type: Article Affiliation country: Spain Country of publication: United kingdom

Full text: 1 Collection: 01-internacional Database: MEDLINE Main subject: Gelsolin / Electron Transport / Voltage-Dependent Anion Channel 1 Limits: Humans Language: En Journal: Hum Mol Genet Journal subject: BIOLOGIA MOLECULAR / GENETICA MEDICA Year: 2017 Document type: Article Affiliation country: Spain Country of publication: United kingdom