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Overexpressing wild-type γ2 subunits rescued the seizure phenotype in Gabrg2+/Q390X Dravet syndrome mice.
Huang, Xuan; Zhou, Chengwen; Tian, Mengnan; Kang, Jing-Qiong; Shen, Wangzhen; Verdier, Kelienne; Pimenta, Aurea; MacDonald, Robert L.
Affiliation
  • Huang X; The Graduate Program of Neuroscience, Vanderbilt University Medical Center, Nashville, Tennessee, U.S.A.
  • Zhou C; Department of Neurology, Vanderbilt University Medical Center, Nashville, Tennessee, U.S.A.
  • Tian M; Department of Neurology, Vanderbilt University Medical Center, Nashville, Tennessee, U.S.A.
  • Kang JQ; Department of Neurology, Vanderbilt University Medical Center, Nashville, Tennessee, U.S.A.
  • Shen W; Department of Neurology, Vanderbilt University Medical Center, Nashville, Tennessee, U.S.A.
  • Verdier K; Department of Neurology, Vanderbilt University Medical Center, Nashville, Tennessee, U.S.A.
  • Pimenta A; Department of Neurology, Vanderbilt University Medical Center, Nashville, Tennessee, U.S.A.
  • MacDonald RL; Department of Neurology, Vanderbilt University Medical Center, Nashville, Tennessee, U.S.A.
Epilepsia ; 58(8): 1451-1461, 2017 08.
Article in En | MEDLINE | ID: mdl-28586508

Full text: 1 Collection: 01-internacional Database: MEDLINE Main subject: Epilepsies, Myoclonic / Receptors, GABA-A / Protein Subunits / Mutation Limits: Animals / Humans / Male Language: En Journal: Epilepsia Year: 2017 Document type: Article Affiliation country: United States

Full text: 1 Collection: 01-internacional Database: MEDLINE Main subject: Epilepsies, Myoclonic / Receptors, GABA-A / Protein Subunits / Mutation Limits: Animals / Humans / Male Language: En Journal: Epilepsia Year: 2017 Document type: Article Affiliation country: United States