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Hypoalphalipoproteinemia and BRAFV600E Mutation Are Major Predictors of Aortic Infiltration in the Erdheim-Chester Disease.
Cohen-Aubart, Fleur; Guerin, Maryse; Poupel, Lucie; Cluzel, Philippe; Saint-Charles, Flora; Charlotte, Frédéric; Arsafi, Youssef; Emile, Jean-François; Frisdal, Eric; Le Goff, Carine; Donadieu, Jean; Amoura, Zahir; Lesnik, Philippe; Haroche, Julien; Le Goff, Wilfried.
Affiliation
  • Cohen-Aubart F; From the Institut E3M, Centre National de Référence des Maladies Rares Auto-Immunes et Systémiques (F.C.-A., Z.A., J.H.).
  • Guerin M; Inserm, Institute of Cardiometabolism and Nutrition (ICAN), UMR_S1166, Hôpital de la Pitié, Sorbonne Université, Paris, France (M.G., F.S.-C., Y.A., E.F., P.L., W.L.G.).
  • Poupel L; Inserm, Institute of Cardiometabolism and Nutrition (ICAN), UMR_S1166, Hôpital de la Pitié, Sorbonne Université, Paris, France (M.G., F.S.-C., Y.A., E.F., P.L., W.L.G.).
  • Cluzel P; Cardiovascular and Interventional Radiology Department (P.C.).
  • Saint-Charles F; Inserm, Institute of Cardiometabolism and Nutrition (ICAN), UMR_S1166, Hôpital de la Pitié, Sorbonne Université, Paris, France (M.G., F.S.-C., Y.A., E.F., P.L., W.L.G.).
  • Charlotte F; Department of Pathology (F.C.).
  • Arsafi Y; Inserm, Institute of Cardiometabolism and Nutrition (ICAN), UMR_S1166, Hôpital de la Pitié, Sorbonne Université, Paris, France (M.G., F.S.-C., Y.A., E.F., P.L., W.L.G.).
  • Emile JF; EA4340, Versailles University, Paris-Saclay University, Boulogne, France (J.-F.E.).
  • Frisdal E; Inserm, Institute of Cardiometabolism and Nutrition (ICAN), UMR_S1166, Hôpital de la Pitié, Sorbonne Université, Paris, France (M.G., F.S.-C., Y.A., E.F., P.L., W.L.G.).
  • Le Goff C; Sorbonne Université, Assistance Publique-Hôpitaux de Paris, Hôpital Pitié-Salpêtrière, France; INSERM UMR1148, Laboratory of Vascular Translational Science, Bichat Hospital, Paris Diderot University, France (C.L.G.).
  • Donadieu J; Haematology Department, Assistance Publique-6-Hôpitaux de Paris, Hôpital Trousseau, France (J.D.).
  • Amoura Z; From the Institut E3M, Centre National de Référence des Maladies Rares Auto-Immunes et Systémiques (F.C.-A., Z.A., J.H.).
  • Lesnik P; Inovarion, Paris, France (L.P.).
  • Haroche J; From the Institut E3M, Centre National de Référence des Maladies Rares Auto-Immunes et Systémiques (F.C.-A., Z.A., J.H.).
  • Le Goff W; Inserm, Institute of Cardiometabolism and Nutrition (ICAN), UMR_S1166, Hôpital de la Pitié, Sorbonne Université, Paris, France (M.G., F.S.-C., Y.A., E.F., P.L., W.L.G.).
Arterioscler Thromb Vasc Biol ; 38(8): 1913-1925, 2018 08.
Article in En | MEDLINE | ID: mdl-29930009

Full text: 1 Collection: 01-internacional Database: MEDLINE Main subject: Aorta / Aortic Diseases / Erdheim-Chester Disease / Proto-Oncogene Proteins B-raf / Hypoalphalipoproteinemias / Histiocytes / Cholesterol, HDL / Mutation Type of study: Diagnostic_studies / Etiology_studies / Observational_studies / Prognostic_studies / Risk_factors_studies Limits: Aged80 Language: En Journal: Arterioscler Thromb Vasc Biol Journal subject: ANGIOLOGIA Year: 2018 Document type: Article

Full text: 1 Collection: 01-internacional Database: MEDLINE Main subject: Aorta / Aortic Diseases / Erdheim-Chester Disease / Proto-Oncogene Proteins B-raf / Hypoalphalipoproteinemias / Histiocytes / Cholesterol, HDL / Mutation Type of study: Diagnostic_studies / Etiology_studies / Observational_studies / Prognostic_studies / Risk_factors_studies Limits: Aged80 Language: En Journal: Arterioscler Thromb Vasc Biol Journal subject: ANGIOLOGIA Year: 2018 Document type: Article