Peripheral neuroblastic tumor of the kidney: case report and review of literature.
Tumori
; 104(6): NP34-NP37, 2018 Dec.
Article
in En
| MEDLINE
| ID: mdl-30021475
ABSTRACT
INTRODUCTION:
Peripheral neuroblastic tumors (PNTs) account for 8%-10% of all pediatric tumors. Adrenal glands and sympathetic ganglia are the commonest site of tumor growth. In the clinicopathologic spectrum of PNTs, neuroblastoma and ganglioneuroma are the most primitive and the most mature tumor form, while ganglioneuroblastoma represents an intermediate state of maturation. Surgical resection is the therapy of choice in localized disease, but can lead to serious complications when performed in the presence of certain imaging-defined risk factors. CASE PRESENTATION We present a rare case of primary intrarenal ganglioneuroblastoma diagnosed in a teenager who underwent conservative surgery and, despite this, developed upper pole renal ischemia without loss of parenchymal function.CONCLUSION:
We underline the complex management of these extremely rare cases of neuroblastic tumors, which require a dedicated multidisciplinary team.Key words
Full text:
1
Collection:
01-internacional
Database:
MEDLINE
Main subject:
Peripheral Nervous System Neoplasms
/
Ganglioneuroblastoma
/
Kidney Neoplasms
/
Neuroblastoma
Type of study:
Risk_factors_studies
Limits:
Adolescent
/
Female
/
Humans
Language:
En
Journal:
Tumori
Year:
2018
Document type:
Article
Affiliation country:
Italy