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Complement activation associated with ADAMTS13 deficiency may contribute to the characteristic glomerular manifestations in Upshaw-Schulman syndrome.
Itami, Hiroe; Hara, Shigeo; Matsumoto, Masanori; Imamura, Shin; Kanai, Rie; Nishiyama, Kei; Ishimura, Masataka; Ohga, Shouichi; Yoshida, Makiko; Tanaka, Ryojiro; Ogawa, Yoshiyuki; Asada, Yujiro; Sekita-Hatakeyama, Yoko; Hatakeyama, Kinta; Ohbayashi, Chiho.
Affiliation
  • Itami H; Department of Diagnostic Pathology, Nara Medical University, Kashihara, Nara, Japan.
  • Hara S; Department of Diagnostic Pathology, Kobe University Graduate School of Medicine, Kobe, Hyogo, Japan.
  • Matsumoto M; Department of Blood Transfusion Medicine, Nara Medical University, Kashihara, Nara, Japan.
  • Imamura S; Internal Medicine, Fukui Red Cross Hospital, Fukui, Fukui, Japan.
  • Kanai R; Department of Pediatrics, Shimane University Faculty of Medicine, Izumo, Shimane, Japan.
  • Nishiyama K; Department of Pediatrics, Graduate School of Medical Sciences, Kyushu University, Fukuoka, Fukuoka, Japan.
  • Ishimura M; Department of Pediatrics, Graduate School of Medical Sciences, Kyushu University, Fukuoka, Fukuoka, Japan.
  • Ohga S; Department of Pediatrics, Graduate School of Medical Sciences, Kyushu University, Fukuoka, Fukuoka, Japan.
  • Yoshida M; Department of Diagnostic Pathology, Hyogo Prefectural Kobe Children's Hospital, Kobe, Hyogo, Japan.
  • Tanaka R; Department of Nephrology, Hyogo Prefectural Kobe Children's Hospital, Kobe, Hyogo, Japan.
  • Ogawa Y; Department of Hematology, Gunma University Graduate School of Medicne, Maebashi, Gunma, Japan.
  • Asada Y; Department of Pathology, Faculty of Medicine, University of Miyazaki, Miyazaki, Miyazaki, Japan.
  • Sekita-Hatakeyama Y; Department of Diagnostic Pathology, Nara Medical University, Kashihara, Nara, Japan.
  • Hatakeyama K; Department of Diagnostic Pathology, Nara Medical University, Kashihara, Nara, Japan. Electronic address: kpathol@naramed-u.ac.jp.
  • Ohbayashi C; Department of Diagnostic Pathology, Nara Medical University, Kashihara, Nara, Japan.
Thromb Res ; 170: 148-155, 2018 10.
Article in En | MEDLINE | ID: mdl-30195146

Full text: 1 Collection: 01-internacional Database: MEDLINE Main subject: Purpura, Thrombotic Thrombocytopenic / ADAMTS13 Protein / Kidney Diseases Type of study: Risk_factors_studies Limits: Adolescent / Adult / Child / Female / Humans / Male Language: En Journal: Thromb Res Year: 2018 Document type: Article Affiliation country: Japan Country of publication: United States

Full text: 1 Collection: 01-internacional Database: MEDLINE Main subject: Purpura, Thrombotic Thrombocytopenic / ADAMTS13 Protein / Kidney Diseases Type of study: Risk_factors_studies Limits: Adolescent / Adult / Child / Female / Humans / Male Language: En Journal: Thromb Res Year: 2018 Document type: Article Affiliation country: Japan Country of publication: United States