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Successful liver transplantation in common variable immune deficiency with reversal of hepatopulmonary syndrome.
Apostolov, Ross; Sinclair, Marie; Lokan, Julie; Angus, Peter.
Affiliation
  • Apostolov R; Liver Transplant Unit, Austin Health, Heidelberg, Victoria, Australia.
  • Sinclair M; Liver Transplant Unit, Austin Health, Heidelberg, Victoria, Australia.
  • Lokan J; Department of Pathology, Austin Health, Heidelberg, Victoria, Australia.
  • Angus P; Liver Transplant Unit, Austin Health, Heidelberg, Victoria, Australia.
BMJ Case Rep ; 12(4)2019 Apr 03.
Article in En | MEDLINE | ID: mdl-30948390
Common variable immune deficiency (CVID) is a primary immunodeficiency disorder that is associated with abnormal liver function tests, however advanced liver disease is uncommon. Hepatopulmonary syndrome (HPS) is a rare but debilitating complication of CVID-associated liver disease. We report a case of CVID complicated by HPS that was successfully treated with orthotopic liver transplant, with the patient recovering to normal hepatic function and successfully weaning off domiciliary oxygen post-transplantation.
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Full text: 1 Collection: 01-internacional Database: MEDLINE Main subject: Liver Transplantation / Common Variable Immunodeficiency / Hepatopulmonary Syndrome Limits: Female / Humans / Middle aged Language: En Journal: BMJ Case Rep Year: 2019 Document type: Article Affiliation country: Australia Country of publication: United kingdom

Full text: 1 Collection: 01-internacional Database: MEDLINE Main subject: Liver Transplantation / Common Variable Immunodeficiency / Hepatopulmonary Syndrome Limits: Female / Humans / Middle aged Language: En Journal: BMJ Case Rep Year: 2019 Document type: Article Affiliation country: Australia Country of publication: United kingdom