Immunoglobulin G-4-Related Retroperitoneal Fibrosis.
J Investig Med High Impact Case Rep
; 9: 23247096211022487, 2021.
Article
in En
| MEDLINE
| ID: mdl-34088232
ABSTRACT
Retroperitoneal fibrosis is caused by the replacement of normal retroperitoneal tissue with fibrosis. The majority of the cases are idiopathic, but some secondary causes include malignancy, infection, drugs, and radiotherapy. Immunoglobulin G-4 (IgG-4) related disease is a relatively newer disease and one of the rarer causes of retroperitoneal fibrosis. It usually involves the pancreas, lungs, kidneys, aorta lacrimal and salivary glands, or extrapancreatic bile duct. Elevated serum IgG-4 is the biomarker of the disease and its levels correlate with disease activity. High-dose glucocorticoid is the treatment of choice.
Key words
Full text:
1
Collection:
01-internacional
Database:
MEDLINE
Main subject:
Retroperitoneal Fibrosis
Type of study:
Diagnostic_studies
/
Etiology_studies
Limits:
Humans
Language:
En
Journal:
J Investig Med High Impact Case Rep
Year:
2021
Document type:
Article
Affiliation country:
United States