Slowly progressive interstitial lung disease preceding typical dermatomyositis symptoms in anti-melanoma differentiation-associated gene 5 antibody-positive clinically amyopathic dermatomyositis.
Respir Med Case Rep
; 34: 101491, 2021.
Article
in En
| MEDLINE
| ID: mdl-34381685
ANCA, cytoplasmic autoantibody; Anti-melanoma differentiation-associated gene 5; BAL, bronchoalveolar lavage; CADM, clinically amyopathic dermatomyositis; CMV, cytomegalovirus; CT, computed tomography; Clinically amyopathic dermatomyositis; DM, dermatomyositis; HRCT, high-resolution computed tomography; ILD, interstitial lung disease; IVCY, intravenous cyclophosphamide; Interstitial lung disease; KL-6, Krebs von den Lungen-6; MDA5, anti-melanoma differentiation-associated gene 5; PSL, prednisolone; PaO2, partial pressure of oxygen; RP-ILD, rapidly progressive interstitial lung disease; SLB, surgical lung biopsy; Slowly progressive; Surgical lung biopsy; TBLB, transbronchial lung biopsy
Full text:
1
Collection:
01-internacional
Database:
MEDLINE
Type of study:
Diagnostic_studies
/
Risk_factors_studies
Language:
En
Journal:
Respir Med Case Rep
Year:
2021
Document type:
Article
Affiliation country:
Japan
Country of publication:
United kingdom