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Genistein improves renal disease in a mouse model of nephropathic cystinosis: a comparison study with cysteamine.
De Leo, Ester; Taranta, Anna; Raso, Roberto; Polishchuk, Elena; D'Oria, Valentina; Pezzullo, Marco; Goffredo, Bianca Maria; Cairoli, Sara; Bellomo, Francesco; Battafarano, Giulia; Camassei, Francesca Diomedi; Del Fattore, Andrea; Polishchuk, Roman; Emma, Francesco; Rega, Laura Rita.
Affiliation
  • De Leo E; Renal Diseases Research Unit, Genetics and Rare Diseases Research Area, Bambino Gesù Children's Hospital, IRCCS, 00146 Rome, Italy.
  • Taranta A; Renal Diseases Research Unit, Genetics and Rare Diseases Research Area, Bambino Gesù Children's Hospital, IRCCS, 00146 Rome, Italy.
  • Raso R; Renal Diseases Research Unit, Genetics and Rare Diseases Research Area, Bambino Gesù Children's Hospital, IRCCS, 00146 Rome, Italy.
  • Polishchuk E; Telethon Institute of Genetics and Medicine, 80078 Pozzuoli, Italy.
  • D'Oria V; Research Laboratories, Confocal Microscopy Core Facility, Bambino Gesù Children's Hospital, IRCCS, 00146 Rome, Italy.
  • Pezzullo M; Core Facilities, Bambino Gesù Children's Hospital, IRCCS, 00146 Rome, Italy.
  • Goffredo BM; Department of Pediatric Specialties and Liver-Kidney Transplantation, Division of Metabolic Biochemistry and Drug Biology, Bambino Gesù Children's Hospital, IRCCS, 00146 Rome, Italy.
  • Cairoli S; Department of Pediatric Specialties and Liver-Kidney Transplantation, Division of Metabolic Biochemistry and Drug Biology, Bambino Gesù Children's Hospital, IRCCS, 00146 Rome, Italy.
  • Bellomo F; Renal Diseases Research Unit, Genetics and Rare Diseases Research Area, Bambino Gesù Children's Hospital, IRCCS, 00146 Rome, Italy.
  • Battafarano G; Bone Physiopathology Research Unit, Genetics and Rare Diseases Research Division, Bambino Gesù Children's Hospital, IRCCS, 00146 Rome, Italy.
  • Camassei FD; Department of Laboratories-Pathology Unit, Bambino Gesù Children's Hospital, 00165 Rome, Italy.
  • Del Fattore A; Bone Physiopathology Research Unit, Genetics and Rare Diseases Research Division, Bambino Gesù Children's Hospital, IRCCS, 00146 Rome, Italy.
  • Polishchuk R; Telethon Institute of Genetics and Medicine, 80078 Pozzuoli, Italy.
  • Emma F; Renal Diseases Research Unit, Genetics and Rare Diseases Research Area, Bambino Gesù Children's Hospital, IRCCS, 00146 Rome, Italy.
  • Rega LR; Division of Nephrology, Department of Pediatric Subspecialties, Bambino Gesù Children's Hospital, IRCCS, 00146 Rome, Italy.
Hum Mol Genet ; 32(7): 1090-1101, 2023 03 20.
Article in En | MEDLINE | ID: mdl-36300303

Full text: 1 Collection: 01-internacional Database: MEDLINE Main subject: Cystinosis / Kidney Diseases Type of study: Prognostic_studies Limits: Animals Language: En Journal: Hum Mol Genet Journal subject: BIOLOGIA MOLECULAR / GENETICA MEDICA Year: 2023 Document type: Article Affiliation country: Italy Country of publication: United kingdom

Full text: 1 Collection: 01-internacional Database: MEDLINE Main subject: Cystinosis / Kidney Diseases Type of study: Prognostic_studies Limits: Animals Language: En Journal: Hum Mol Genet Journal subject: BIOLOGIA MOLECULAR / GENETICA MEDICA Year: 2023 Document type: Article Affiliation country: Italy Country of publication: United kingdom