Surgical excision of a giant retroperitoneal liposarcoma with renal cell carcinoma: A case report of the largest retroperitoneal sarcoma.

INTRODUCTION: Retroperitoneal liposarcomas are rare malignant tumors known for their slow growth and challenging management, particularly due to their substantial size upon diagnosis. This case report highlights a remarkable instance of a massive retroperitoneal sarcoma concomitant with synchronous renal cell carcinoma. CASE PRESENTATION: We report a 57-year-old male patient with a huge abdominal mass hampering his daily activities and on further investigation, CECT abdomen and pelvis revealed a large Retroperitoneal Scarcoma (RPS) occupying his entire abdominal cavity displacing the visceral organs. In accordance with the final decision of the multi-disciplinary team meeting, he was subjected for surgery and the tumor was excised enbloc. He is kept under surveillance. DISCUSSION: Surgery remains the main modality of treatment for RPS. Hence careful preoperative surgical planning and execution with meticulous dissection aids in achieving a good clinical outcome and to reduce recurrence in future. CONCLUSION: Despite the huge size of the tumor, surgical intervention remains the primary treatment option whenever feasible, often complemented by additional therapeutic approaches.