A chylothorax in a young woman: The difficulties of medical management.
Respirol Case Rep
; 12(2): e01303, 2024 Feb.
Article
in En
| MEDLINE
| ID: mdl-38371459
ABSTRACT
Lymphangioleiomyomatosis is a rare pulmonary disease affecting women of childbearing age. Whilst chylothorax is a well-recognized complication of the condition, management strategies aren't well-defined, have low success rates and are often only available at tertiary or specialist centres. We describe a case of a young woman referred to pleural clinic with a chylous effusion found to be secondary to lymphangioleiomyomatosis. Initial medical management was unsuccessful and recurrent drainages caused significant complications. Remission was ultimately achieved with a combination of mTOR inhibitors and interventional radiology techniques.
Full text:
1
Collection:
01-internacional
Database:
MEDLINE
Language:
En
Journal:
Respirol Case Rep
Year:
2024
Document type:
Article
Country of publication:
United States