Treatment of Klippel-Feil syndrome with symptomatic atlantoaxial instability in a 7-year-old boy : A case report.
Orthopadie (Heidelb)
; 53(10): 799-804, 2024 Oct.
Article
in En
| MEDLINE
| ID: mdl-39117750
ABSTRACT
Klippel-Feil syndrome (KFS) is a congenital deformity of the cervical spine. Clinical symptoms of KFS are reduced range of motion, short neck and low hairline. In adult KFS patients the deformity can lead to adjacent segmental instability with spinal canal stenosis, radiculopathy and myelopathy. This article reports about the diagnostics and treatment management of juvenile KFS patient with myelopathy due to instability of the C1/C2 segment, subsequent stenosis through the posterior arch of C1 and symptomatic myelopathy. This 7year-old boy could be successfully treated with C1 decompression and computer tomography (CT) guided C1/C2 stabilization with pedicle screws under intraoperative neuromonitoring.
Key words
Full text:
1
Collection:
01-internacional
Database:
MEDLINE
Main subject:
Atlanto-Axial Joint
/
Joint Instability
/
Klippel-Feil Syndrome
Limits:
Child
/
Humans
/
Male
Language:
En
Journal:
Orthopadie (Heidelb)
Year:
2024
Document type:
Article
Affiliation country:
Germany
Country of publication:
Germany