Mice deficient in all forms of lysosomal beta-hexosaminidase show mucopolysaccharidosis-like pathology.

Suzuki, K; Sango, K; Proia, R L; Langaman, C

Suzuki, K; Sango, K; Proia, R L; Langaman, C.

Affiliation

Suzuki K; Department of Pathology & Laboratory Medicine, School of Medicine, University of North Carolina at Chapel Hill 27599-7525, USA.

J Neuropathol Exp Neurol ; 56(6): 693-703, 1997 Jun.

Article in En | MEDLINE | ID: mdl-9184660

Subject(s)

Lysosomes/enzymology; Mucopolysaccharidoses/enzymology; beta-N-Acetylhexosaminidases/deficiency; Animals; Brain/enzymology; Brain/ultrastructure; Disease Models, Animal; Glycosaminoglycans/metabolism; Mice; Mice, Mutant Strains; Mucopolysaccharidoses/genetics; Mucopolysaccharidoses/pathology; Peripheral Nerves/enzymology; Peripheral Nerves/ultrastructure; beta-N-Acetylhexosaminidases/genetics

Search on Google

Add to My VHL

XML

PubMed Links

Collection: 01-internacional Database: MEDLINE Main subject: Beta-N-Acetylhexosaminidases / Mucopolysaccharidoses / Lysosomes Type of study: Prognostic_studies Limits: Animals Language: En Journal: J Neuropathol Exp Neurol Year: 1997 Document type: Article Affiliation country: United States Country of publication: United kingdom

Search on Google

Add to My VHL

XML

PubMed Links