Foveal cone dysfunction syndrome.
J Neuroophthalmol
; 18(1): 9-14, 1998 Mar.
Article
in En
| MEDLINE
| ID: mdl-9532531
ABSTRACT
Our objective was to describe and expand the clinical spectrum of a rarely detected, previously reported photoreceptor disorder restricted to the foveal cones. Three patients with bilaterally decreased acuity and hemeralopia were examined to exclude a structural, vascular, inflammatory, or degenerative process. Each patient underwent a full neuroophthalmic examination, including full-field and focal cone electroretinogram (ERG). All three patients had normal-appearing fundi, mild dyschromatopsia, central or paracentral visual field depressions, normal full-field photopic and scotopic ERGs, and markedly reduced focal, foveal cone ERG responses. One patient had a ring scotoma and an asymptomatic family member with abnormal full-field and focal cone ERG. The syndrome of acquired foveal cone dysfunction presents as a bilateral, painless, progressive central visual loss with minimal or absent fundus changes. It eludes diagnosis until focal, foveal cone ERG is performed.
Search on Google
Collection:
01-internacional
Database:
MEDLINE
Main subject:
Retinal Diseases
/
Retinal Cone Photoreceptor Cells
/
Fovea Centralis
Type of study:
Diagnostic_studies
Limits:
Aged
/
Female
/
Humans
/
Male
/
Middle aged
Language:
En
Journal:
J Neuroophthalmol
Journal subject:
NEUROLOGIA
/
OFTALMOLOGIA
Year:
1998
Document type:
Article
Affiliation country:
United States