A severe acute intermittent porphyria patient: Successful treatment and management / 中华内分泌代谢杂志
Chinese Journal of Endocrinology and Metabolism
; (12): 335-338, 2022.
Article
in Zh
| WPRIM
| ID: wpr-933411
Responsible library:
WPRO
ABSTRACT
Acute intermittent porphyria(AIP) is a rare inherited metabolic disease that can cause severe and fatal acute attacks. This article shares the treatment and management of a severe AIP patient. It is proposed that (1) avoiding incentives is essential; (2) emotional problems easily overlooked should be paid attention; (3) long-term follow-up and patient education can improve the prognosis. The patient underwent renal biopsy during the remission period. We found a red-brown-yellow-white refractive index crystal under a polarized light microscope that had not been reported in the previous literature, which was speculated to be a porphyrin crystal.
Full text:
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Database:
WPRIM
Language:
Zh
Journal:
Chinese Journal of Endocrinology and Metabolism
Year:
2022
Document type:
Article