Uterine cavity embryonal rhabdomyosarcoma
Autops. Case Rep
; 9(3): e2019104, July-Sept. 2019. ilus
Artículo
en Inglés
| LILACS
| ID: biblio-1017386
Biblioteca responsable:
BR26.7
ABSTRACT
Rhabdomyosarcoma (RMS) is a rare solid tumor in childhood and adolescence. The higher incidence is predominant during the first two decades of life. According to the Intergroup RMS Study Group, the embryonal RMS (ERMS), botryoidal variant, constitutes a histological subtype characterized as a "grape-like" lesion of 2.0 cm to 9.5 cm. The treatment involves chemotherapy, surgery, and/or radiotherapy. We present the case of a 14-year-old female patient diagnosed with ERMS, botryoidal variant, which originated in the uterine cervix with vaginal externalization. The initial therapeutic approach comprised an initial prolapsed mass excision followed by WertheimMeigs surgery due to the tumor extension. No consensual protocol to ERMS treatment is found in the medical literature; however, a combined approach seems to offer a better result. The postoperative time period was uneventful and the patient followed an adjuvant therapy with vincristine, d-actinomycin, and cyclophosphamide. A comprehensive evaluation of the therapeutic options preserving the reproductive functionunfortunately not always possibleis part of a multi-disciplined care team concerning the pediatric patients.
Texto completo:
Disponible
Colección:
Bases de datos internacionales
Base de datos:
LILACS
Asunto principal:
Neoplasias del Cuello Uterino
/
Rabdomiosarcoma Embrionario
Tipo de estudio:
Guía de práctica clínica
Límite:
Adolescente
/
Femenino
/
Humanos
Idioma:
Inglés
Revista:
Autops. Case Rep
Asunto de la revista:
Anatomia
/
Patologia Cl¡nica
/
Patologia Legal
Año:
2019
Tipo del documento:
Artículo
País de afiliación:
Brasil
Institución/País de afiliación:
Centro Universitário Lusíada/BR
/
Hospital Ana Costa/BR
/
Hospital Guilherme Álvaro/BR