Rare association between atrioventricular septal defect and partial anomalous pulmonary venous connection

ABSTRACT

Abstract Clinical data Infant, 7 months, female, referred to our department at one month of age, suspecting of congenital heart disease for further investigation. Chest radiography Demonstrates cardiomegaly and prominent pulmonary vascular markings. Electrocardiography Shows right ventricular hypertrophy and left anterior fascicular block. Echocardiography Evidenced common atrioventricular valve with two orifices and the left superior pulmonary vein draining on the brachiocephalic vein. Computed tomography angiography This complementary imaging exam was performed to confirm the diagnosis. Diagnosis The patient presented an association between AVSD and PAPVC, a rare combination. The clinical picture of heart failure was preponderant, characterized by need for diuretics and complementary exams findings, and early surgical treatment was indicated. Operation The operation was performed through a median sternotomy with 123 minutes of cardiopulmonary bypass and 89 minutes of cross-clamping time. The patient had no postoperative complications, remaining 10 days hospitalized.