Erythrocyte alkaline phosphatase in patients with myotonic muscle disorders / Fosfatasa alcalina en eritrocitos de pacientes con enfermedades musculares miotónicas
Invest. clín
; 37(4): 247-53, dic. 1996. ilus
Artículo
en Español
| LILACS
| ID: lil-199243
Biblioteca responsable:
VE1.1
ABSTRACT
The allosteric behavior of the p-nitrophenyl-phosphatase (EC.3.1.3.1) from membrane erythrocytes was investigated in the following mulltisystemic diseases myotonic dystrophy limb-girdle muscular dystrophy, Charcot-Marie-Tooth and juvenile spinal muscular atrophy; in myotonia congenita. which is not a multisystemic disease, and in healthy controls. The Hill coefficient in F-inhibition in controls was different from that in multisystemic diseases patients but not from that in myotonia congenita patients. Changes in the cooperative type kinetics would suggest that the interaction membrane-enzyme in controls and in patients with neuromuscular disorders is only different for multisystemic diseases
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Colección:
Bases de datos internacionales
Base de datos:
LILACS
Asunto principal:
Enfermedad de Charcot-Marie-Tooth
/
Fosfatasa Alcalina
/
Eritrocitos
/
Enfermedades Musculares
/
Distrofias Musculares
Límite:
Femenino
/
Humanos
/
Masculino
Idioma:
Español
Revista:
Invest. clín
Asunto de la revista:
Biologia
/
Medicina
/
Relatos de Casos
Año:
1996
Tipo del documento:
Artículo