Neurocutaneous melanosis associated with Dandy-Walker malformation. case report and review of the literature.
Pediatr Neurosurg
; 33(5): 270-273, 2000 Nov.
Article
en En
| MEDLINE
| ID: mdl-11155066
ABSTRACT
Neurocutaneous melanosis is a rare dysmorphogenesis associated with single or multiple giant pigmented cutaneous nevi and diffuse involvement of the leptomeninges anywhere in the central nervous system (CNS). It is interesting that almost 8-10% of patients had associated Dandy-Walker malformation in the literature, suggesting a common origin of the developmental abnormalities. In this article, we present a 2-year-old patient with neurocutaneous melanosis associated with Dandy-Walker malformation. We reviewed the literature and discuss the pathogenesis based on the preferred hypotheses so far.
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Colección:
01-internacional
Base de datos:
MEDLINE
Asunto principal:
Síndromes Neurocutáneos
/
Síndrome de Dandy-Walker
/
Melanosis
Tipo de estudio:
Diagnostic_studies
/
Risk_factors_studies
Límite:
Child, preschool
/
Humans
/
Male
Idioma:
En
Revista:
Pediatr Neurosurg
Asunto de la revista:
NEUROCIRURGIA
/
PEDIATRIA
Año:
2000
Tipo del documento:
Article
País de afiliación:
Turquía