[Space occupying lesion of unknown origin in the pulmonary trunk: targeted differential diagnosis and surgical therapy in a patient with B symptoms and thoracic pain]. / Unklare Raumforderung im Truncus pulmonalis: Gezielte Differenzialdiagnostik und chirurgische Therapie bei einem Patienten mit B-Symptomatik und Thoraxschmerzen.

Leiomyosarcomas are only rarely found in routine cardiac surgery. For the patient they hold, however, a very high-risk potential as only an early diagnosis, and immediate surgical therapy leads to long-term survival. Awareness, timely diagnosis, and immediate radical surgical therapy is imperative. This report describes the case of a 21-year old male with a strong suspicion of leiomyosarcoma of the pulmonary artery. Due to his clinical symptoms, the patient was transferred to operation immediately after completion of all diagnostic measurements. Postoperatively the diagnosis of a leiomyosarcoma proved to be false; instead a rare fibro-histologic tumor was found. Even in the case of a suspected leiomyosarcoma, rapid and radical surgical therapy is imperative due to the poor prognosis of leiomyosarcoma.